ICD-10-CM code · FY2027
E71.510 Zellweger syndrome
BillableValid for claims as a specific diagnosis code
About E71.510
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Coding notes for E71.510
No notes of its own; the notes below apply from the codes above it.
Also applies, from E71.51 Disorders of peroxisome biogenesis
Excludes1 Not coded here: never report these together with this code (use the code given instead).
- Refsum's disease (G60.1)
Also applies, from E71.5 Peroxisomal disorders
Excludes1 Not coded here: never report these together with this code (use the code given instead).
- Schilder's disease (G37.0)
Block E70-E88 notes (apply to every code in it)
Excludes1 Not coded here: never report these together with this code (use the code given instead).
Excludes2 Not part of this condition, but a patient can have both: report both codes when both apply.
- Ehlers-Danlos syndromes (Q79.6-)
Chapter 4 notes (apply to every code in it)
Note
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Related codes in E71.51
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See 2MM+ plansICD-10-CM FY2027 code set, as published by the CDC National Center for Health Statistics (NCHS) and CMS, effective October 1, 2026 to September 30, 2027. Codes, titles and notes are shown as published. Check payer rules and the official guidelines before billing. This page is not medical advice.
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