ICD-10-CM code · FY2027
E76 Disorders of glycosaminoglycan metabolism
Header codeNot billable: use one of the 12 billable codes below
About E76
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Coding notes for E76
No notes of its own.
Block E70-E88 notes (apply to every code in it)
Excludes1 Not coded here: never report these together with this code (use the code given instead).
Excludes2 Not part of this condition, but a patient can have both: report both codes when both apply.
- Ehlers-Danlos syndromes (Q79.6-)
Chapter 4 notes (apply to every code in it)
Note
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Codes under E76 15
- E76.0 Mucopolysaccharidosis, type IHeader
- E76.01 Hurler's syndromeBillable
- E76.02 Hurler-Scheie syndromeBillable
- E76.03 Scheie's syndromeBillable
- E76.1 Mucopolysaccharidosis, type IIBillable
- E76.2 Other mucopolysaccharidosesHeader
- E76.21 Morquio mucopolysaccharidosesHeader
- E76.210 Morquio A mucopolysaccharidosesBillable
- E76.211 Morquio B mucopolysaccharidosesBillable
- E76.219 Morquio mucopolysaccharidoses, unspecifiedBillable
- E76.22 Sanfilippo mucopolysaccharidosesBillable
- E76.29 Other mucopolysaccharidosesBillable
- E76.3 Mucopolysaccharidosis, unspecifiedBillable
- E76.8 Other disorders of glucosaminoglycan metabolismBillable
- E76.9 Glucosaminoglycan metabolism disorder, unspecifiedBillable
Other categories in E70-E88
- E70 Disorders of aromatic amino-acid metabolismHeader
- E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolismHeader
- E72 Other disorders of amino-acid metabolismHeader
- E73 Lactose intoleranceHeader
- E74 Other disorders of carbohydrate metabolismHeader
- E75 Disorders of sphingolipid metabolism and other lipid storage disordersHeader
- E77 Disorders of glycoprotein metabolismHeader
- E78 Disorders of lipoprotein metabolism and other lipidemiasHeader
- E79 Disorders of purine and pyrimidine metabolismHeader
- E80 Disorders of porphyrin and bilirubin metabolismHeader
- E83 Disorders of mineral metabolismHeader
- E84 Cystic fibrosisHeader
- E85 AmyloidosisHeader
- E86 Volume depletionHeader
- E87 Other disorders of fluid, electrolyte and acid-base balanceHeader
- E88 Other and unspecified metabolic disordersHeader
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See 2MM+ plansICD-10-CM FY2027 code set, as published by the CDC National Center for Health Statistics (NCHS) and CMS, effective October 1, 2026 to September 30, 2027. Codes, titles and notes are shown as published. Check payer rules and the official guidelines before billing. This page is not medical advice.
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