ICD-10-CM code · FY2027
E84.0 Cystic fibrosis with pulmonary manifestations
BillableValid for claims as a specific diagnosis code
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Coding notes for E84.0
Use additional code Add a second code for the detail named here.
- code to identify any infectious organism present, such as:
- Pseudomonas (B96.5)
Also applies, from E84 Cystic fibrosis
Includes Conditions this code covers.
- mucoviscidosis
Code also Another code may be needed as well; the order depends on the encounter.
- exocrine pancreatic insufficiency (K86.81)
Block E70-E88 notes (apply to every code in it)
Excludes1 Not coded here: never report these together with this code (use the code given instead).
Excludes2 Not part of this condition, but a patient can have both: report both codes when both apply.
- Ehlers-Danlos syndromes (Q79.6-)
Chapter 4 notes (apply to every code in it)
Note
- All neoplasms, whether functionally active or not, are classified in Chapter 2. Appropriate codes in this chapter (i.e. E05.8, E07.0, E16-E31, E34.-) may be used as additional codes to indicate either functional activity by neoplasms and ectopic endocrine tissue or hyperfunction and hypofunction of endocrine glands associated with neoplasms and other conditions classified elsewhere.
Related codes in E84
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See 2MM+ plansICD-10-CM FY2027 code set, as published by the CDC National Center for Health Statistics (NCHS) and CMS, effective October 1, 2026 to September 30, 2027. Codes, titles and notes are shown as published. Check payer rules and the official guidelines before billing. This page is not medical advice.